妊娠期合并噬血细胞综合征是产科的危急重症,起病较隐匿,进展快,病情凶险,甚至危及生命。目的:通过总结讨论1例妊娠合并噬血细胞综合征早期识别、诊疗经过,为临床提供经验和借鉴。方法:回顾性分析一例妊娠合并噬血细胞综合征的临床资料。结论:妊娠期有不明原因的高热、肝酶升高患者,应将噬血细胞综合征疾病考虑在内,及早完善铁蛋白、脾脏超声等辅助检查,可尽早明确诊断。一经确诊需立即救治,及时终止妊娠,随后可继续血液科治疗,为母婴安全保驾护航。Hemophagocytic syndrome during pregnancy is a critical and severe condition in obstetrics. The onset is hidden, the progress is rapid, and the condition is dangerous and even life-threatening. Objective: To provide clinical experience and reference by summarizing and discussing the early identification, diagnosis and treatment of a case of pregnancy complicated with hemophagocytic syndrome. Methods: The clinical data of a case of pregnancy complicated with hemophagocytic syndrome were analyzed retrospectively. Conclusion: Hemophagocytic syndrome should be taken into account in patients with unexplained high fever and elevated liver enzymes during pregnancy, and auxiliary examination of ferritin and spleen ultrasound should be improved as soon as possible to make a clear diagnosis. Once diagnosed, it is necessary to immediately treat, terminate pregnancy in time, and then continue hematology treatment to escort the safety of mother and child.
