目的:探讨无痛性泪腺腺样囊性癌(Adenoid cystic carcinoma of lacrimal gland, LGACC)的临床特征,以提升对该罕见肿瘤的认识。方法:回顾性分析1例LGACC患者的临床资料,并结合国内外文献进行复习探讨。结果:患者因发现左眼进行性突出伴上睑下垂就诊,无疼痛等不适,影像学检查提示左眼眶内肿物,行眶内肿物摘除术,病理诊断为腺样囊性癌。术后接受全身化疗,随访6月未见肿瘤复发或转移。结论:无痛性泪腺腺样囊性癌罕见,因解剖位置隐匿导致诊断困难,需尽早手术干预并结合病理明确诊断。Objective: To investigate the clinical features of painless adenoid cystic carcinoma of lacrimal gland (LGACC) in order to improve the understanding of this rare tumor. Methods: The clinical data of 1 patient with LGACC of lacrimal gland adenoid cystic carcinoma were analyzed retrospectively, and the literature at home and abroad was reviewed. Results: The patient presented with progressive proptosis of the left eye accompanied by ptosis, without experiencing pain or other discomfort. Imaging examination revealed left orbital mass and resection of orbital mass was performed. The postoperative pathology revealed adenoid cystic carcinoma. The patients received systemic chemotherapy after surgery, and no tumor recurrence or metastasis was found in 36 months of follow-up. Conclusion: Painless adenoid cystic carcinoma of lacrimal gland is rare and difficult to diagnose due to hidden anatomical location. Early surgical intervention and pathological diagnosis are necessary.
